アブストラクト（32巻1号：The Bulletin of Kanagawa Dental College）

The Bulletin of Kanagawa Dental College

English

Title　： Pachydermoperiostosis : Report of a Rare Case with Possible Oral Manifestations
Subtitle　： ORIGINAL ARTICLES
Authors　： Ilknur Ozcan*, Zuhal Yurdabakan*, Deniz Firat**, Sinan Soley**, Yigit Sirin**, Nahide Onsun***
Authors（kana）　：
Organization　： *University of Istanbul, Faculty of Dentistry, Department of Oral Diagnosis & Radiology, **University of Istanbul, Faculty of Dentistry, Department of Oral Surgery, ***Vakif Gureba Hospital, Clinic of Dermatology, Istanbul
Journal　： The Bulletin of Kanagawa Dental College
Volume　： 32
Number　： 1
Page　： 3-7
Year/Month　： 2004 / 3
Article　： Original article
Publisher　： Kanagawa Odontological Society
Abstract　： [Abstract] Pachydermoperiostosis is a rare syndrome characterized by the presence of various hypertrophic skin changes such as clubbing of the fingers, coarse facial features, cutis verticis gyrata of the scalp and seborrhea. Cortical thickening of long bones and periosteal new bone formation are also reported in most of the cases. We aim to describe a 43 year-old female patient diagnosed as having primary pacyhdermoperiostosis complete form with a swelling in the left maxillary region and chronic pain in the temporomandibular joint area. Panoramic radiography revealed a well-circumscribed sclerotic cortical bone lesion 1 cm in diameter in the left maxillary tuber region. The lesion was removed with the neighboring cortical bone. Microscopic examination of the surgical specimen revealed relatively dense, compact bone with sparse marrow tissue diagnosed as osteoma of the maxilla. Although many cases in different countries have been reported in medical literature about this rare developmental disease, there is a lack of studies concerning oral manifestations such as possible bone abnormalities and soft tissue reactions. Moreover, female cases are relatively rare depending on the prevalence of this disorder. A possible correlation between osteoma formation and typical periosteal reactions of this disease is discussed along with their effects on the oral hard and soft tissues.
Practice　： Dentistry
Keywords　： Pachydermoperiostosis, Soft tissue hypertrophy, Periosteal bone formation